Tag: Alkaptonuria diet

Alkaptonuria is a rare metabolic disorder affecting approximately 1 in 250,000 people globally. Proper dietary management is critical to address what should be restricted in alkaptonuria, focusing on the metabolism of certain amino acids.

Alkaptonuria (AKU) is a rare inherited metabolic disorder, affecting approximately 1 in 250,000 to 1 million people worldwide, that prevents the complete breakdown of two amino acids: phenylalanine and tyrosine. For individuals with this condition, understanding **what foods should you avoid if you have alkaptonuria?** is a critical part of managing their health and preventing complications from the resulting build-up of homogentisic acid (HGA).