Tag: Glycogen storage disease

According to research, a high-protein, low-carbohydrate diet combined with exercise may help improve symptoms in some individuals with Late-Onset Pompe Disease (LOPD). Understanding what is the diet for Pompe disease is a crucial component of overall management alongside enzyme replacement therapy (ERT).

According to a study published in the journal *Midwifery*, more than 5% of expectant mothers in a large group of Brazilians reported craving and eating non-food items. This behavior, known as pica, is one of the primary reasons people eat cornstarch, though nutritional and psychological factors also play a significant role.

According to sports science, the average person stores approximately 400 grams of glycogen in their muscles and liver, but what happens if you have no glycogen? When these carbohydrate stores are exhausted, the body enters a state of crisis, triggering a cascade of metabolic changes to find alternative energy sources. This can have profound effects on physical performance, cognitive function, and overall health.

According to the USDA, a single cup of commercial cornstarch contains 488 calories but offers little to no fiber or protein. This nutrient-sparse profile has led many to question: does eating cornstarch have any benefits for your health?

A compulsive craving for non-food items like raw starch, known medically as amylophagia, is often a symptom of an underlying medical condition called pica. This behavior, where individuals may eat corn starch powder directly from the box, is a complex phenomenon with multiple potential causes that go beyond simple appetite.

According to research published in the *Journal of Strength and Conditioning Research*, a significant number of athletes experience gastrointestinal issues from glycogen supplements. While popular for performance enhancement, this raises important questions about the safety and suitability of these products for the general population.

According to the Muscular Dystrophy Association, Pompe disease, a severe form of acid maltase deficiency, is a rare genetic disorder that results in profound muscle weakness. This article explores what happens if you lack maltase, detailing the symptoms, causes, and consequences of this enzyme deficiency.

Did you know that symptoms of low maltase can present in two distinct forms: either as a digestive disorder or a progressive muscular condition? Low maltase can cause gastrointestinal discomfort from carbohydrate malabsorption or serious, progressive muscle weakness depending on the specific enzyme deficiency.

According to the Cleveland Clinic, the compulsive craving for non-food items like cornstarch, a disorder known as pica, is often linked to underlying medical issues, most notably iron-deficiency anemia. Understanding **why would someone want to eat cornstarch** is critical to differentiating a simple craving from a potentially serious health condition requiring professional attention.

For decades, the administration of uncooked cornstarch has been a cornerstone for managing severe fasting hypoglycemia in patients with glycogen storage diseases (GSD). What is the cornstarch protocol? It is a specialized medical nutrition strategy designed to provide a slow, steady release of glucose into the bloodstream over several hours.