Tag: Special formulas

According to the National Institutes of Health, phenylketonuria (PKU) is an inherited disorder that prevents the body from properly processing the amino acid phenylalanine. This makes understanding dietary restrictions critical, so the question arises: can I eat peanut butter with PKU? The answer is a clear no, as peanut butter is a high-protein food containing high levels of phenylalanine.

Phenylketonuria (PKU) affects approximately 1 in 25,000 newborns in the United States, making newborn screening vital for early diagnosis. A phenylketonuria free diet is the primary treatment for this genetic disorder, preventing the buildup of a harmful amino acid called phenylalanine. This specialized, lifelong eating plan restricts high-protein foods while ensuring adequate nutrition through medical formulas and careful food choices.

Hereditary tyrosinemia affects approximately 1 in 100,000 people globally and requires strict dietary management to control tyrosine levels. Understanding what foods are good for tyrosinemia is crucial, as a carefully controlled low-protein diet is the cornerstone of treatment alongside medication like nitisinone. This nutritional guide provides comprehensive information on which foods are safe and which should be avoided to help manage this complex metabolic disorder.